Prion Disease

Name:

Candidate number:

Theme:

 

OPTION LIST

 

A	Huntington’s Disease	I	Stroke
B	Kuru	J	Encephalitis
C	Cerebral Vasculitis	K	Creutzfeldt-Jakob Disease
D	Iatrogenic CJD	L	Gerstmann-Straussler-Sheinker Syndrome
E	Paraneoplastic Syndrome	M	Variant CJD
F	Familial Fatal Insomnia	N
G	Schizophrenia	O
H	Alzheimer’s Disease	P

 

For each scenario below, choose the most appropriate answer from the list above. Each option may be used once, more than once or not at all.

 

1. A 40-year old male motorcyclist presents with paranoid hallucinations and peripheral sensory symptoms. MRI brain shows positive pulvinar sign.

 

 

2. A 60-year old male presents with progressive and sudden jerky movement. The only previous medical history of note for the patient is a corneal operation 9 years previously.

 

 

3. An 80-year old lady from Papua New Guinea presents with myoclonus.

 

 

4. A 70-year old male presents with rapid dementia associated with cortical blindness.EEG shows periodic triphasic complexes.

 

 

5. A 50-year old woman presents with slowly progressive ataxia. On examination reflexes were found to be diminished. The woman has expressed concern as her mother died of a similar condition.

 

ANSWERS

1. M

2. D

3. B

4. K

5. L