Pathology EMQ template.

Name: Alice Hope                

Candidate number:

Theme: Haemolytic Anaemia

 

OPTION LIST

 

A

Glucose-6-phosphate deficiency

I

Microangiopathic haemolytic anaemia

B

Hereditary elliptocytosis

J

 

C

Pyruvate kinase deficiency

K

 

D

Sickle cell disease

L

 

E

Hereditary spherocytosis

M

 

F

Β-Thalassaemia

N

 

G

Haemolytic disease of the newborn

O

 

H

Autoimmune haemolytic anaemia

P

 

 

 

For each scenario below, choose the most appropriate answer from the list above. Each option may be used once, more than once or not at all.

 

1.   A five year old boy presents with a history of jaundice and tiredness.  On examination there is mild splenomegally. A Hb of 9 is found.  On the blood film there are a number of small rounded cells. 

 

2. A 13 year old girl presents with a fever, cough and malaise.  Blood cultures show an infection with Haemophilis influenzae.  She has also had admissions previously for hand and foot pain. 

 

 

3. A 6 year old boy presents with jaundice and anaemia following eating fava beans.

 

 

4. A 5month old boy presents with jaundice and severe anaemia.  His parents are also worried that he is not growing and putting on weight.  On examination you find hepatosplenomegally and a prominent jaw.

 

 

5. A newborn baby boy is noticed to have jaundice.  There is no hepatosplenogmegally and the Hb is only mildly low.  Both parents are rhesus positive.  Coombs test is positive.

 

 

ANSWERS

1. E

2. D

3. A

4. F

5. G